A 58-year-old Hispanic woman had decreased visual acuity in the left eye for 3 years and intermittent episodes of pain and red eye. On examination, her best-corrected visual acuity was 20/20 OD and light perception OS. She had diffuse nevus flammeus involving the left upper eyelid, cheek, and nose, suggestive of Sturge-Weber syndrome. The anterior segment of the left eye demonstrated dilated and tortuous conjunctival vessels, clear cornea, shallow anterior chamber, and normal iris. The intraocular pressure was 27 mm Hg OS, and fundus examination showed exudative retinal detachment in the left eye (Figure 1A) with shifting fluid. Fluorescein angiography (Figure 1B) demonstrated early diffuse hyperfluorescence and late hypofluorescence, and optical coherence tomography (Figure 1C) confirmed the presence of subretinal fluid. B-scan ultrasonography confirmed diffuse thickening of the choroid and an exudative retinal detachment with A-scan high internal reflectivity of the choroidal mass (Figure 1D), corresponding with the diagnosis of a DCH.