In 2010, the patient was referred to our institution with a history of gradually recurrent proptosis and recent-onset diplopia. Orbital imaging demonstrated a large, homogeneously enhancing mass that filled the inferotemporal extraconal and intraconal left orbit (Figure 1). A lower fornix-approach orbitotomy was performed with removal of all gross tumor (Figure 2). Histologic sections showed a proliferation of spindle cells with eosinophilic cytoplasm, poorly defined cytoplasmic borders, and elongated nuclei with small eosinophilic nucleoli, arranged in short intersecting fascicles in a “patternless pattern” (Figure 3A). Occasional hemangiopericytic thin-walled vessels were present (Figure 3B). Rare mitotic figures were seen, with no atypical forms, areas of necrosis, or cytologic atypia identified. Immunohistochemical staining revealed that neoplastic cells were strongly and diffusely positive for CD34 (Figure 3C), CD99, and Bcl-2 and negative for smooth muscle actin, muscle-specific actin, desmin, S-100 protein, and AE1/AE3 cytokeratins, supporting the diagnosis of SFT. The patient did well following gross tumor excision and remained symptom free at 1 year.