Chondromyxoid fibroma with orbital involvement has been reported only in brief case reports.4- 6 Hashimoto et al4 and Cruz et al5 described a CMF of the ethmoid sinus destroying the medial orbital wall. Wolf et al6 reported an intracranial CMF of the frontal-sphenoid junction with secondary orbital involvement. In our patient, there was—to our knowledge for the first time—marked downward displacement and indentation of the globe with choroidal folds caused by progressive orbital tumor growth. Because the adjacent periosteum was intact, we elected to take an extraperiosteal approach, separating tumor and periosteum from bone as much as possible. In the area of close adhesion to the adjacent frontal bone, an en bloc resection including the tumor, surrounding periosteum, and adjacent bony wall was performed. Complete en bloc resection is important regarding both histopathological diagnosis and the prevention of tumor recurrence. Simple curettage may favor underdiagnosis and explain in part why the entity has been rarely documented.