Unilateral, sclerosing, follicular, lymphoid hyperplasia of the submandibular gland (Küttner tumor) is an immunophenotypically polyclonal process with a favorable prognosis. It is typically unassociated with systemic disease and rarely encountered with dacryoadenitis.1- 3 The submandibular and lacrimal diseases can be linked through the recently characterized spectrum of IgG4-positive sclerosing inflammatory diseases,3,4 which we documented in the biopsies of our patient's 2 lesions. Concomitant serological elevation of IgG4 levels may develop5,6; it was not evaluated in our patient but should probably be sought in orbital pseudotumors. Other IgG4-related diseases include autoimmune pancreatitis, sclerosing orbital inflammatory disease, Riedel struma, and retroperitoneal fibrosis.7 IgG4-positive disease is highly sensitive to corticosteroid therapy. The role of IgG4-positive plasma cells in fibrosclerosis is unknown.