Slitlamp examination revealed 11 corneas with peripheral opacities concentric with the limbus resembling but less sharply defined than a typical embryotoxon posterior (III:20, IV:1, IV:7, IV:10, V:1, and V:4). Individual III:20 had bilateral primary open-angle glaucoma. Gonioscopy performed in 3 other patients (IV:10, V:1, and V:7) revealed normal angles. Slight correctopia and iris hypoplasia were observed in all of the eyes (Figure 2). Eleven eyes (III:20, IV:1, IV:6, IV:7, IV:9, and IV:10) underwent cataract surgery. In addition, bilateral cataracts were observed in individuals V:1, V:4, and V:7. One eye in individual IV:1 was amaurotic due to retinal detachment. Individual V:1 had a nonsymptomatic retinal detachment in the left eye. Both eyes were myopic, at −7 and −10. Neither eye had undergone previous surgery. Retinal detachment after cataract surgery was reported previously1 in 2 other affected family members (III:2 and III:16) (Figure 1). Examination of the fundus showed foveal hypoplasia in all of the eyes (Figure 3).